棕榈酰辅酶 A 的β-氧化
中文名称
通路描述
由α-氧化产生的棕榈酰辅酶 A 在过氧化物酶体中进一步经历三个β-氧化循环，生成4,8-二甲基壬酰辅酶 A、乙酰辅酶 A 和两个丙酰辅酶 A。这些分子随后转化为辅酶 A 结合辅因子，可转运至线粒体（Wanders and Waterham 2006, Verhoeven et al. 1998, Ferdinandusse et al. 1999）。
英文描述
Beta-oxidation of pristanoyl-CoA Pristanoyl-CoA, generated in the peroxisome by alpha-oxidation of dietary phytanic acid, is further catabolized by three cycles of peroxisomal beta-oxidation to yield 4,8-dimethylnonanoyl-CoA, acetyl-CoA and two molecules of propionyl-CoA. These molecules in turn are converted to carnitine conjugates, which can be transported to mitochondria (Wanders and Waterham 2006, Verhoeven et al. 1998, Ferdinandusse et al. 1999).
所含基因
8 个基因