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Peroxisomal lipid metabolism

Reactome ID: R-HSA-390918

中文名称

过氧化物酶体脂质代谢

通路描述

在人类中,植物酸、棕榈酸和长链脂肪酸的分解代谢以及磷脂酰胆碱的前四个合成步骤由过氧化物酶体酶催化。任何这些酶的缺陷或过氧化物酶体的组装缺陷都与严重的发育障碍相关(Wanders and Watherham 2006)。
英文描述
Peroxisomal lipid metabolism In humans, the catabolism of phytanate, pristanate, and very long chain fatty acids as well as the first four steps of the biosynthesis of plasmalogens are catalyzed by peroxisomal enzymes. Defects in any of these enzymes or in the assembly of peroxisomes are associated with severe developmental disorders (Wanders and Watherham 2006).

所含基因

5 个基因