肉豆蔻酰-CoA到肉豆蔻酰-CoA的β-氧化
中文名称
通路描述
第一次通过β-氧化螺旋的β-氧化始于饱和脂肪酸肉豆蔻酰-CoA，产生肉豆蔻酰-CoA。需要四个酶促步骤，起始于长链酰-CoA脱氢酶（VLCAD）活性，随后是三个酶促步骤：烯酰-CoA水合酶、3-羟基酰-CoA脱氢酶和酮酰-CoA硫解酶活性，这些活性均存在于与线粒体膜相关的三功能蛋白中。
英文描述
Beta oxidation of palmitoyl-CoA to myristoyl-CoA This first pass through the beta-oxidation spiral starts with the saturated fatty acid palmitoyl-CoA and produces myristoyl-CoA. Four enzymatic steps are required, starting with VLCAD CoA dehydrogenase (Very Long Chain) activity, followed by three enzymatic steps, enoyl-CoA hydratase, 3-hydroxyacyl-CoA dehydrogenase, and ketoacyl-CoA thiolase activities, all present in the mitochondrial membrane associated trifunctional protein.
所含基因
3 个基因