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Aminoacyl-tRNA biosynthesis

KEGG ID: hsa00970

中文名称

氨酰-tRNA 生物合成

通路描述

氨酰-tRNA 生物合成通过 ATP 为每种氨酰-tRNA 合成酶提供其特异性氨基酸,确保 mRNA 向蛋白质的准确翻译;错误会导致氨基酸掺入错误,引起蛋白质功能障碍和细胞应激。
英文描述
Aminoacyl-tRNA biosynthesis charges each aminoacyl-tRNA synthetase with its cognate amino acid using ATP, ensuring accurate translation of mRNA into proteins; errors lead to misincorporation causing protein dysfunction and cellular stress.

所含基因

489 个基因
AARS1 AARS2 CARS1 CARS2 DARS1 DARS2 EARS2 EPRS1 FARS2 FARSA FARSB GARS1 GATB GATC HARS1 HARS2 IARS1 IARS2 KARS1 LARS1 LARS2 MARS1 MARS2 MTFMT NARS1 NARS2 PARS2 PSTK QARS1 QRSL1 RARS1 RARS2 SARS1 SARS2 SEPSECS TARS1 TARS2 TARS3 TRA-AGC1-1 TRA-AGC10-1 TRA-AGC11-1 TRA-AGC12-1 TRA-AGC12-3 TRA-AGC13-2 TRA-AGC14-1 TRA-AGC14-2 TRA-AGC15-1 TRA-AGC2-1 TRA-AGC2-2 TRA-AGC24-1 TRA-AGC3-1 TRA-AGC4-1 TRA-AGC5-1 TRA-AGC6-1 TRA-AGC7-1 TRA-AGC8-1 TRA-AGC8-2 TRA-AGC9-1 TRA-CGC1-1 TRA-CGC2-1 TRA-CGC3-1 TRA-CGC4-1 TRA-CGC5-1 TRA-TGC1-1 TRA-TGC2-1 TRA-TGC3-1 TRA-TGC3-2 TRA-TGC4-1 TRA-TGC5-1 TRA-TGC6-1 TRA-TGC7-1 TRC-GCA1-1 TRC-GCA10-1 TRC-GCA11-1 TRC-GCA12-1 TRC-GCA13-1 TRC-GCA14-1 TRC-GCA15-1 TRC-GCA16-1 TRC-GCA17-1 TRC-GCA18-1 TRC-GCA19-1 TRC-GCA2-1 TRC-GCA2-2 TRC-GCA2-3 TRC-GCA2-4 TRC-GCA20-1 TRC-GCA21-1 TRC-GCA22-1 TRC-GCA23-1 TRC-GCA3-1 TRC-GCA4-1 TRC-GCA5-1 TRC-GCA6-1 TRC-GCA7-1 TRC-GCA8-1 TRC-GCA9-1 TRC-GCA9-2 TRC-GCA9-3 TRC-GCA9-4 TRD-GTC1-1 TRD-GTC2-1 TRD-GTC2-10 TRD-GTC2-11 TRD-GTC2-2 TRD-GTC2-3 TRD-GTC2-4 TRD-GTC2-5 TRD-GTC2-6 TRD-GTC2-7 TRD-GTC2-8 TRD-GTC2-9 TRD-GTC3-1 TRE-CTC1-1 TRE-CTC1-2 TRE-CTC1-3 TRE-CTC1-4 TRE-CTC1-5 TRE-CTC1-6 TRE-CTC1-7 TRE-CTC2-1 TRE-TTC1-1 TRE-TTC1-2 TRE-TTC2-1 TRE-TTC2-2 TRE-TTC3-1 TRE-TTC4-1 TRE-TTC4-2 TRF-GAA1-1 TRF-GAA1-2 TRF-GAA1-3 TRF-GAA1-4 TRF-GAA1-5 TRF-GAA1-6 TRF-GAA2-1 TRF-GAA3-1 TRF-GAA4-1 TRF-GAA5-1 TRF-GAA6-1 TRG-CCC1-1 TRG-CCC1-2 TRG-CCC2-1 TRG-CCC2-2 TRG-CCC3-1 TRG-CCC4-1 TRG-CCC5-1 TRG-CCC6-1 TRG-GCC1-1 TRG-GCC1-2 TRG-GCC1-3 TRG-GCC1-4 TRG-GCC1-5 TRG-GCC2-1 TRG-GCC2-2 TRG-GCC2-3 TRG-GCC2-4 TRG-GCC2-5 TRG-GCC2-6 TRG-GCC3-1 TRG-GCC4-1 TRG-TCC1-1 TRG-TCC2-1 TRG-TCC2-2 TRG-TCC2-3 TRG-TCC2-4 TRG-TCC2-5 TRG-TCC2-6 TRG-TCC3-1 TRG-TCC4-1 TRH-GTG1-1 TRH-GTG1-2 TRH-GTG1-3 TRH-GTG1-4 TRH-GTG1-5 TRH-GTG1-6 TRH-GTG1-7 TRH-GTG1-8 TRH-GTG1-9 TRI-AAT1-1 TRI-AAT2-1 TRI-AAT3-1 TRI-AAT4-1 TRI-AAT5-1 TRI-AAT5-2 TRI-AAT5-3 TRI-AAT5-4 TRI-AAT5-5 TRI-AAT6-1 TRI-AAT7-1 TRI-AAT7-2 TRI-AAT8-1 TRI-AAT9-1 TRI-GAT1-1 TRI-GAT1-2 TRI-GAT1-3 TRI-TAT1-1 TRI-TAT2-1 TRI-TAT2-2 TRI-TAT2-3 TRI-TAT3-1 TRK-CTT1-1 TRK-CTT1-2 TRK-CTT2-1 TRK-CTT2-2 TRK-CTT2-3 TRK-CTT2-4 TRK-CTT2-5 TRK-CTT3-1 TRK-CTT4-1 TRK-CTT5-1 TRK-CTT6-1 TRK-CTT7-1 TRK-CTT8-1 TRK-CTT9-1 TRK-TTT1-1 TRK-TTT2-1 TRK-TTT3-1 TRK-TTT3-2 TRK-TTT3-3 TRK-TTT3-4 TRK-TTT3-5 TRK-TTT4-1 TRK-TTT5-1 TRK-TTT6-1 TRK-TTT7-1 TRK-TTT8-1 TRK-TTT9-1 TRL-AAG1-1 TRL-AAG1-2 TRL-AAG1-3 TRL-AAG2-1 TRL-AAG2-2 TRL-AAG2-3 TRL-AAG2-4 TRL-AAG3-1 TRL-AAG4-1 TRL-CAA1-1 TRL-CAA1-2 TRL-CAA2-1 TRL-CAA3-1 TRL-CAA4-1 TRL-CAA6-1 TRL-CAG1-1 TRL-CAG1-2 TRL-CAG1-3 TRL-CAG1-4 TRL-CAG1-5 TRL-CAG1-6 TRL-CAG1-7 TRL-CAG2-1 TRL-CAG2-2 TRL-TAA1-1 TRL-TAA2-1 TRL-TAA3-1 TRL-TAA4-1 TRL-TAG1-1 TRL-TAG2-1 TRL-TAG3-1 TRM-CAT1-1 TRM-CAT2-1 TRM-CAT3-1 TRM-CAT3-2 TRM-CAT4-1 TRM-CAT4-2 TRM-CAT4-3 TRM-CAT5-1 TRM-CAT5-2 TRM-CAT6-1 TRM-CAT7-1 TRN-GTT1-1 TRN-GTT10-1 TRN-GTT2-1 TRN-GTT2-2 TRN-GTT2-3 TRN-GTT2-4 TRN-GTT2-5 TRN-GTT2-6 TRN-GTT2-7 TRN-GTT2-8 TRN-GTT24-1 TRN-GTT25-1 TRN-GTT26-1 TRN-GTT27-1 TRN-GTT3-1 TRN-GTT4-1 TRN-GTT5-1 TRN-GTT6-1 TRN-GTT7-1 TRN-GTT8-1 TRN-GTT9-1 TRN-GTT9-2 TRNA TRNAA-AGC TRNAE-UUC TRNAG-CCC TRNAI-AAU TRNAN-GUU TRNAV-CAC TRNC TRND TRNE TRNF TRNG TRNH TRNI TRNK TRNL1 TRNL2 TRNM TRNN TRNP TRNQ TRNR TRNS1 TRNS2 TRNT TRNV TRNW TRNY TRP-AGG1-1 TRP-AGG2-1 TRP-AGG2-2 TRP-AGG2-3 TRP-AGG2-4 TRP-AGG2-5 TRP-AGG2-6 TRP-AGG2-7 TRP-AGG2-8 TRP-CGG1-1 TRP-CGG1-2 TRP-CGG1-3 TRP-CGG2-1 TRP-TGG1-1 TRP-TGG2-1 TRP-TGG3-1 TRP-TGG3-2 TRP-TGG3-3 TRP-TGG3-4 TRP-TGG3-5 TRQ-CTG1-1 TRQ-CTG1-2 TRQ-CTG1-3 TRQ-CTG1-4 TRQ-CTG1-5 TRQ-CTG2-1 TRQ-CTG3-1 TRQ-CTG3-2 TRQ-CTG4-1 TRQ-CTG4-2 TRQ-CTG5-1 TRQ-CTG6-1 TRQ-CTG7-1 TRQ-TTG1-1 TRQ-TTG2-1 TRQ-TTG3-1 TRQ-TTG3-2 TRQ-TTG3-3 TRQ-TTG4-1 TRR-ACG1-1 TRR-ACG1-2 TRR-ACG1-3 TRR-ACG2-1 TRR-ACG2-2 TRR-ACG2-3 TRR-ACG2-4 TRR-CCG1-1 TRR-CCG1-2 TRR-CCG1-3 TRR-CCG2-1 TRR-CCT1-1 TRR-CCT2-1 TRR-CCT3-1 TRR-CCT4-1 TRR-TCG1-1 TRR-TCG2-1 TRR-TCG3-1 TRR-TCG4-1 TRR-TCG5-1 TRR-TCT1-1 TRR-TCT2-1 TRR-TCT3-1 TRR-TCT3-2 TRR-TCT4-1 TRR-TCT5-1 TRS-AGA1-1 TRS-AGA2-1 TRS-AGA2-2 TRS-AGA2-3 TRS-AGA2-4 TRS-AGA2-5 TRS-AGA2-6 TRS-AGA3-1 TRS-AGA4-1 TRS-AGA5-1 TRS-CGA1-1 TRS-CGA2-1 TRS-CGA3-1 TRS-CGA4-1 TRS-GCT1-1 TRS-GCT3-1 TRS-GCT4-1 TRS-GCT4-2 TRS-GCT4-3 TRS-GCT5-1 TRS-GCT6-1 TRS-TGA1-1 TRS-TGA2-1 TRS-TGA3-1 TRS-TGA4-1 TRT-AGT1-1 TRT-AGT1-2 TRT-AGT1-3 TRT-AGT2-1 TRT-AGT2-2 TRT-AGT3-1 TRT-AGT4-1 TRT-AGT5-1 TRT-AGT6-1 TRT-CGT1-1 TRT-CGT3-1 TRT-TGT1-1 TRT-TGT2-1 TRT-TGT3-1 TRT-TGT4-1 TRT-TGT6-1 TRU-TCA1-1 TRU-TCA2-1 TRV-AAC1-1 TRV-AAC1-2 TRV-AAC1-3 TRV-AAC1-4 TRV-AAC1-5 TRV-AAC2-1 TRV-AAC3-1 TRV-AAC4-1 TRV-AAC5-1 TRV-AAC6-1 TRV-CAC1-1 TRV-CAC1-2 TRV-CAC1-3 TRV-CAC1-4 TRV-CAC1-5 TRV-CAC1-6 TRV-CAC1-7 TRV-CAC2-1 TRV-CAC3-1 TRV-CAC4-1 TRV-CAC5-1 TRV-CAC6-1 TRV-CAC8-1 TRV-TAC1-1 TRV-TAC1-2 TRV-TAC2-1 TRV-TAC3-1 TRV-TAC4-1 TRW-CCA1-1 TRW-CCA2-1 TRW-CCA3-1 TRW-CCA3-2 TRW-CCA3-3 TRW-CCA4-1 TRW-CCA5-1 TRX-CAT1-1 TRX-CAT1-2 TRX-CAT1-3 TRX-CAT1-4 TRX-CAT1-5 TRX-CAT1-6 TRX-CAT1-7 TRX-CAT1-8 TRY-ATA1-1 TRY-GTA1-1 TRY-GTA2-1 TRY-GTA3-1 TRY-GTA4-1 TRY-GTA5-1 TRY-GTA5-2 TRY-GTA5-3 TRY-GTA5-4 TRY-GTA5-5 TRY-GTA6-1 TRY-GTA7-1 TRY-GTA8-1 VARS1 VARS2 WARS1 WARS2 YARS1 YARS2