氨酰-tRNA 生物合成
中文名称
通路描述
氨酰-tRNA 生物合成通过 ATP 为每种氨酰-tRNA 合成酶提供其特异性氨基酸,确保 mRNA 向蛋白质的准确翻译;错误会导致氨基酸掺入错误,引起蛋白质功能障碍和细胞应激。
英文描述
Aminoacyl-tRNA biosynthesis charges each aminoacyl-tRNA synthetase with its cognate amino acid using ATP, ensuring accurate translation of mRNA into proteins; errors lead to misincorporation causing protein dysfunction and cellular stress.
所含基因
489 个基因
AARS1
AARS2
CARS1
CARS2
DARS1
DARS2
EARS2
EPRS1
FARS2
FARSA
FARSB
GARS1
GATB
GATC
HARS1
HARS2
IARS1
IARS2
KARS1
LARS1
LARS2
MARS1
MARS2
MTFMT
NARS1
NARS2
PARS2
PSTK
QARS1
QRSL1
RARS1
RARS2
SARS1
SARS2
SEPSECS
TARS1
TARS2
TARS3
TRA-AGC1-1
TRA-AGC10-1
TRA-AGC11-1
TRA-AGC12-1
TRA-AGC12-3
TRA-AGC13-2
TRA-AGC14-1
TRA-AGC14-2
TRA-AGC15-1
TRA-AGC2-1
TRA-AGC2-2
TRA-AGC24-1
TRA-AGC3-1
TRA-AGC4-1
TRA-AGC5-1
TRA-AGC6-1
TRA-AGC7-1
TRA-AGC8-1
TRA-AGC8-2
TRA-AGC9-1
TRA-CGC1-1
TRA-CGC2-1
TRA-CGC3-1
TRA-CGC4-1
TRA-CGC5-1
TRA-TGC1-1
TRA-TGC2-1
TRA-TGC3-1
TRA-TGC3-2
TRA-TGC4-1
TRA-TGC5-1
TRA-TGC6-1
TRA-TGC7-1
TRC-GCA1-1
TRC-GCA10-1
TRC-GCA11-1
TRC-GCA12-1
TRC-GCA13-1
TRC-GCA14-1
TRC-GCA15-1
TRC-GCA16-1
TRC-GCA17-1
TRC-GCA18-1
TRC-GCA19-1
TRC-GCA2-1
TRC-GCA2-2
TRC-GCA2-3
TRC-GCA2-4
TRC-GCA20-1
TRC-GCA21-1
TRC-GCA22-1
TRC-GCA23-1
TRC-GCA3-1
TRC-GCA4-1
TRC-GCA5-1
TRC-GCA6-1
TRC-GCA7-1
TRC-GCA8-1
TRC-GCA9-1
TRC-GCA9-2
TRC-GCA9-3
TRC-GCA9-4
TRD-GTC1-1
TRD-GTC2-1
TRD-GTC2-10
TRD-GTC2-11
TRD-GTC2-2
TRD-GTC2-3
TRD-GTC2-4
TRD-GTC2-5
TRD-GTC2-6
TRD-GTC2-7
TRD-GTC2-8
TRD-GTC2-9
TRD-GTC3-1
TRE-CTC1-1
TRE-CTC1-2
TRE-CTC1-3
TRE-CTC1-4
TRE-CTC1-5
TRE-CTC1-6
TRE-CTC1-7
TRE-CTC2-1
TRE-TTC1-1
TRE-TTC1-2
TRE-TTC2-1
TRE-TTC2-2
TRE-TTC3-1
TRE-TTC4-1
TRE-TTC4-2
TRF-GAA1-1
TRF-GAA1-2
TRF-GAA1-3
TRF-GAA1-4
TRF-GAA1-5
TRF-GAA1-6
TRF-GAA2-1
TRF-GAA3-1
TRF-GAA4-1
TRF-GAA5-1
TRF-GAA6-1
TRG-CCC1-1
TRG-CCC1-2
TRG-CCC2-1
TRG-CCC2-2
TRG-CCC3-1
TRG-CCC4-1
TRG-CCC5-1
TRG-CCC6-1
TRG-GCC1-1
TRG-GCC1-2
TRG-GCC1-3
TRG-GCC1-4
TRG-GCC1-5
TRG-GCC2-1
TRG-GCC2-2
TRG-GCC2-3
TRG-GCC2-4
TRG-GCC2-5
TRG-GCC2-6
TRG-GCC3-1
TRG-GCC4-1
TRG-TCC1-1
TRG-TCC2-1
TRG-TCC2-2
TRG-TCC2-3
TRG-TCC2-4
TRG-TCC2-5
TRG-TCC2-6
TRG-TCC3-1
TRG-TCC4-1
TRH-GTG1-1
TRH-GTG1-2
TRH-GTG1-3
TRH-GTG1-4
TRH-GTG1-5
TRH-GTG1-6
TRH-GTG1-7
TRH-GTG1-8
TRH-GTG1-9
TRI-AAT1-1
TRI-AAT2-1
TRI-AAT3-1
TRI-AAT4-1
TRI-AAT5-1
TRI-AAT5-2
TRI-AAT5-3
TRI-AAT5-4
TRI-AAT5-5
TRI-AAT6-1
TRI-AAT7-1
TRI-AAT7-2
TRI-AAT8-1
TRI-AAT9-1
TRI-GAT1-1
TRI-GAT1-2
TRI-GAT1-3
TRI-TAT1-1
TRI-TAT2-1
TRI-TAT2-2
TRI-TAT2-3
TRI-TAT3-1
TRK-CTT1-1
TRK-CTT1-2
TRK-CTT2-1
TRK-CTT2-2
TRK-CTT2-3
TRK-CTT2-4
TRK-CTT2-5
TRK-CTT3-1
TRK-CTT4-1
TRK-CTT5-1
TRK-CTT6-1
TRK-CTT7-1
TRK-CTT8-1
TRK-CTT9-1
TRK-TTT1-1
TRK-TTT2-1
TRK-TTT3-1
TRK-TTT3-2
TRK-TTT3-3
TRK-TTT3-4
TRK-TTT3-5
TRK-TTT4-1
TRK-TTT5-1
TRK-TTT6-1
TRK-TTT7-1
TRK-TTT8-1
TRK-TTT9-1
TRL-AAG1-1
TRL-AAG1-2
TRL-AAG1-3
TRL-AAG2-1
TRL-AAG2-2
TRL-AAG2-3
TRL-AAG2-4
TRL-AAG3-1
TRL-AAG4-1
TRL-CAA1-1
TRL-CAA1-2
TRL-CAA2-1
TRL-CAA3-1
TRL-CAA4-1
TRL-CAA6-1
TRL-CAG1-1
TRL-CAG1-2
TRL-CAG1-3
TRL-CAG1-4
TRL-CAG1-5
TRL-CAG1-6
TRL-CAG1-7
TRL-CAG2-1
TRL-CAG2-2
TRL-TAA1-1
TRL-TAA2-1
TRL-TAA3-1
TRL-TAA4-1
TRL-TAG1-1
TRL-TAG2-1
TRL-TAG3-1
TRM-CAT1-1
TRM-CAT2-1
TRM-CAT3-1
TRM-CAT3-2
TRM-CAT4-1
TRM-CAT4-2
TRM-CAT4-3
TRM-CAT5-1
TRM-CAT5-2
TRM-CAT6-1
TRM-CAT7-1
TRN-GTT1-1
TRN-GTT10-1
TRN-GTT2-1
TRN-GTT2-2
TRN-GTT2-3
TRN-GTT2-4
TRN-GTT2-5
TRN-GTT2-6
TRN-GTT2-7
TRN-GTT2-8
TRN-GTT24-1
TRN-GTT25-1
TRN-GTT26-1
TRN-GTT27-1
TRN-GTT3-1
TRN-GTT4-1
TRN-GTT5-1
TRN-GTT6-1
TRN-GTT7-1
TRN-GTT8-1
TRN-GTT9-1
TRN-GTT9-2
TRNA
TRNAA-AGC
TRNAE-UUC
TRNAG-CCC
TRNAI-AAU
TRNAN-GUU
TRNAV-CAC
TRNC
TRND
TRNE
TRNF
TRNG
TRNH
TRNI
TRNK
TRNL1
TRNL2
TRNM
TRNN
TRNP
TRNQ
TRNR
TRNS1
TRNS2
TRNT
TRNV
TRNW
TRNY
TRP-AGG1-1
TRP-AGG2-1
TRP-AGG2-2
TRP-AGG2-3
TRP-AGG2-4
TRP-AGG2-5
TRP-AGG2-6
TRP-AGG2-7
TRP-AGG2-8
TRP-CGG1-1
TRP-CGG1-2
TRP-CGG1-3
TRP-CGG2-1
TRP-TGG1-1
TRP-TGG2-1
TRP-TGG3-1
TRP-TGG3-2
TRP-TGG3-3
TRP-TGG3-4
TRP-TGG3-5
TRQ-CTG1-1
TRQ-CTG1-2
TRQ-CTG1-3
TRQ-CTG1-4
TRQ-CTG1-5
TRQ-CTG2-1
TRQ-CTG3-1
TRQ-CTG3-2
TRQ-CTG4-1
TRQ-CTG4-2
TRQ-CTG5-1
TRQ-CTG6-1
TRQ-CTG7-1
TRQ-TTG1-1
TRQ-TTG2-1
TRQ-TTG3-1
TRQ-TTG3-2
TRQ-TTG3-3
TRQ-TTG4-1
TRR-ACG1-1
TRR-ACG1-2
TRR-ACG1-3
TRR-ACG2-1
TRR-ACG2-2
TRR-ACG2-3
TRR-ACG2-4
TRR-CCG1-1
TRR-CCG1-2
TRR-CCG1-3
TRR-CCG2-1
TRR-CCT1-1
TRR-CCT2-1
TRR-CCT3-1
TRR-CCT4-1
TRR-TCG1-1
TRR-TCG2-1
TRR-TCG3-1
TRR-TCG4-1
TRR-TCG5-1
TRR-TCT1-1
TRR-TCT2-1
TRR-TCT3-1
TRR-TCT3-2
TRR-TCT4-1
TRR-TCT5-1
TRS-AGA1-1
TRS-AGA2-1
TRS-AGA2-2
TRS-AGA2-3
TRS-AGA2-4
TRS-AGA2-5
TRS-AGA2-6
TRS-AGA3-1
TRS-AGA4-1
TRS-AGA5-1
TRS-CGA1-1
TRS-CGA2-1
TRS-CGA3-1
TRS-CGA4-1
TRS-GCT1-1
TRS-GCT3-1
TRS-GCT4-1
TRS-GCT4-2
TRS-GCT4-3
TRS-GCT5-1
TRS-GCT6-1
TRS-TGA1-1
TRS-TGA2-1
TRS-TGA3-1
TRS-TGA4-1
TRT-AGT1-1
TRT-AGT1-2
TRT-AGT1-3
TRT-AGT2-1
TRT-AGT2-2
TRT-AGT3-1
TRT-AGT4-1
TRT-AGT5-1
TRT-AGT6-1
TRT-CGT1-1
TRT-CGT3-1
TRT-TGT1-1
TRT-TGT2-1
TRT-TGT3-1
TRT-TGT4-1
TRT-TGT6-1
TRU-TCA1-1
TRU-TCA2-1
TRV-AAC1-1
TRV-AAC1-2
TRV-AAC1-3
TRV-AAC1-4
TRV-AAC1-5
TRV-AAC2-1
TRV-AAC3-1
TRV-AAC4-1
TRV-AAC5-1
TRV-AAC6-1
TRV-CAC1-1
TRV-CAC1-2
TRV-CAC1-3
TRV-CAC1-4
TRV-CAC1-5
TRV-CAC1-6
TRV-CAC1-7
TRV-CAC2-1
TRV-CAC3-1
TRV-CAC4-1
TRV-CAC5-1
TRV-CAC6-1
TRV-CAC8-1
TRV-TAC1-1
TRV-TAC1-2
TRV-TAC2-1
TRV-TAC3-1
TRV-TAC4-1
TRW-CCA1-1
TRW-CCA2-1
TRW-CCA3-1
TRW-CCA3-2
TRW-CCA3-3
TRW-CCA4-1
TRW-CCA5-1
TRX-CAT1-1
TRX-CAT1-2
TRX-CAT1-3
TRX-CAT1-4
TRX-CAT1-5
TRX-CAT1-6
TRX-CAT1-7
TRX-CAT1-8
TRY-ATA1-1
TRY-GTA1-1
TRY-GTA2-1
TRY-GTA3-1
TRY-GTA4-1
TRY-GTA5-1
TRY-GTA5-2
TRY-GTA5-3
TRY-GTA5-4
TRY-GTA5-5
TRY-GTA6-1
TRY-GTA7-1
TRY-GTA8-1
VARS1
VARS2
WARS1
WARS2
YARS1
YARS2